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Lookzadeh, M., Tabatabaie, R., Saeida- Ardekani, M., Bakhshayesh, H. (2022). A Case Report of Neurocutaneous Melanosis with Associated Dandy-Walker Complex. Shahid Sadoughi University of Medical Sciences- Journal Management System, 5(2), 96-98. doi: 10.18502/wjpn.v5i2.11996
Mohamad Hosein Lookzadeh; Razieh Sadat Tabatabaie; Maryam Saeida- Ardekani; Hanie Bakhshayesh. "A Case Report of Neurocutaneous Melanosis with Associated Dandy-Walker Complex". Shahid Sadoughi University of Medical Sciences- Journal Management System, 5, 2, 2022, 96-98. doi: 10.18502/wjpn.v5i2.11996
Lookzadeh, M., Tabatabaie, R., Saeida- Ardekani, M., Bakhshayesh, H. (2022). 'A Case Report of Neurocutaneous Melanosis with Associated Dandy-Walker Complex', Shahid Sadoughi University of Medical Sciences- Journal Management System, 5(2), pp. 96-98. doi: 10.18502/wjpn.v5i2.11996
Lookzadeh, M., Tabatabaie, R., Saeida- Ardekani, M., Bakhshayesh, H. A Case Report of Neurocutaneous Melanosis with Associated Dandy-Walker Complex. Shahid Sadoughi University of Medical Sciences- Journal Management System, 2022; 5(2): 96-98. doi: 10.18502/wjpn.v5i2.11996

A Case Report of Neurocutaneous Melanosis with Associated Dandy-Walker Complex

World Journal of Peri and Neonatology
Article 6, Volume 5, Issue 2, December 2022, Pages 96-98    PDF (275.46 K)
Document Type: Case Report
DOI: 10.18502/wjpn.v5i2.11996
Authors
Mohamad Hosein Lookzadeh1; Razieh Sadat Tabatabaie2; Maryam Saeida- Ardekani1; Hanie Bakhshayesh* 3
1Mother and Newborn Health Research Center, Shahid Sadoughi University of Medical Sciences, Yazd, Iran
2Department of Obstetrics and Gynecology, Shahid Sadoughi University of Medical Sciences, Yazd, Iran
3Department of Pediatrics, Shahid Sadoughi University of Medical Sciences, Yazd, Iran
Abstract
Background: Neurocutaneous melanosis (NCM) and Dandy-Walker malformation (DWM) are two forms of rare congenital neurodysplasia. NCM is a rare dysmorphogenesis characterized by single or multiple giants pigmented cutaneous nevi and the involvement of benign and/or malignant melanocytic tumors of the leptomeninges. DWM is a rare congenital malformation of the brain. Cystic enlargement of the fourth ventricle is its characteristic that communicates with an enlarged posterior fossa, cerebellar dysgenesis, high tentorial insertion, and hydrocephalus. However, these two conditions are rare, and NCM associated with DWC is even more unusual.
Case Report: Here, we report a male newborn with macrocephaly and multiple pigmented nevi over his whole body with regular borders and normal weight, height, and spine. He was finally diagnosed as NCM in association with DWC.
Conclusion: After diagnosing NCM in association with DWC, appropriate follow-up is recommended; however, there is no particular treatment to prevent the malignant change.
Keywords
Neurocutaneous melanosis; Dandy-Walker malformation; Dysmorphogenesis; Neurocutaneous syndrome; Melanoma
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